ESPU Congress 2017 - Abstract book

292

CONGRESS OF THE ESPU

VS-18 (VS without presentation)

THE ASSOCIATION OF CONGENITAL URETHRAL

DUPLICATION AND MEGALOURETHRA

Ahsen KARAGOZLU AKGUL, Murat UCAR, Nizamettin KILIC and Emin BALKAN

Uludag University Faculty of Medicine, Department of Pediatric Surgery, Division of Pediatric Urology, Bursa, TURKEY

PURPOSE

Congenital megalourethra and urethral duplication are rare urogenital malformations. Congenital

megalourethra characterized by severe dilatation and elongation of the penile urethra. The clinical

presentations of congenital urethral duplications may vary due to anatomical differences. The condi-

tion is usually diagnosed in childhood due to the presence of duplicated urethral meatus or from

double stream if both are functional. In older ages, the condition is diagnosed from complications

that trigger infections or obstruction or further complications if it is associated with more extensive

malformations. In this case, urethral duplication was diagnosed in new-born period and both ure-

thras were in form of megalourethra.

MATERIAL AND METHODS

The 10-month-old baby presented with penile swelling during voiding that recognized by his par-

ents. Physical examination revealed a retractable foreskin, two external meatus of double urethra.

Retrograde urethrographic and urethroscopic evaluation demonstrated urethral duplication with

megalourethra.

RESULTS

Excision of the ventral megalourethra, tapering of dorsally placed megalourethra and urethroplasty

were performed.

The details of the procedure was presented as a video.

CONCLUSIONS

Urethral duplication with megalourethra is an extremely rare birth defect. As our knowledge it is the

first case with complete duplicated megalourethra in the literature. The treatment of the urethral

duplication with megalourethra should be individualized according to the type of duplication and the

clinical symptoms.

VS-19 (VS without presentation)

FEMALE EPISPADIAS REPAIR:

THE TRANSPUBIC‑PERINEAL APPROACH

Paolo CAIONE

, Simona GEROCARNI NAPPO

and Michele INNOCENZI

1) Bambino Gesu Hospital, Paediatric Urology, Rome, ITALY - 2) Bambino Gesù Children's Hospital, Division

of Paediatric Urology, Rome, ITALY

PURPOSE

Female epispadias (FE), the least severe defect of the exstrophy complex, is referred as very

uncommon (1:480.000 female live born). It involves the urethra and partially the bladder neck (BN)

with consequent urinary incontinence. Surgical repair is controversial with partially satisfying results.

We present our transpubic-perineal approach.

MATERIAL AND METHODS

In lithotomic position, a 3 cm "inverted Y" incision was carried out from suprapubic midline to labia

majora internal aspect. The epispadic urethral plate was mobilized between the bifid clitoris. The

midline incision was depth into the retropubic space. Bladder neck and urethra were sagittally

split. "Z-plasties" allowed to elongate and narrow the bladder neck and urethra on a 7-Ch catheter.