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29

th

CONGRESS OF THE ESPU

RESULTS

Four patients were male and 6 of the 7 presented with gross hematuria. Ultrasound (US) was the

most common imaging modality, showing an intravesical polyps mainly in the trigone. MRI was

performed in 4 cases and revealed a mass with heterogeneous low-intermediate signal intensity in

T1 and T2-weighted sequence. All the lesions were solitary. Transurethral resection of the bladder

wall was performed in all cases. Histological studies showed grade-I TCCB (urothelial papilloma)

in all cases, and one patient had two recurrences with a final histological result showing grade-II

TCCB, treated with installation of Amyticine. All patients were alive with no evidence of disease after

a median follow-up of 8.3 years.

CONCLUSIONS

Urothelial tumors are likely to manifest as hematuria, occur as solitary lesions and are gener-

ally low grade. These lesions have low recurrence potential with extremely favorable prognoses.

Endoscopic treatment in urothelial tumor proved effective, with the necessity of a regular follow up

either by US or cystoscopy in atypical aspect.

14:08–14:10

S2-5 (CP)

TRANSIENT PSEUDOHYPOALDOSTERONISM:

A POTENTIALLY SEVERE CONDITION AFFECTING INFANTS

WITH URINARY TRACT MALFORMATION

Xavier DELFORGE 

1

, Elodie HARAUX 

1

, Axelle CAULIEZ 

2

, Karine BRAUN 

2

,

Guy KONGOLO 

3

and Philippe BUISSON 

1

1) CHU Amiens, Pediatric surgery, Amiens, FRANCE - 2) CHU Amiens, Pediatric endocrinology, Amiens, FRANCE -

3) CHU Amiens, Pediatric intensive care unit, Amiens, FRANCE

PURPOSE

Secondary pseudohypoaldosteronism (S-PHA) is a life-threatening condition affecting young chil-

dren with urinary tract malformation (UTM), but remains unfamiliar to pediatric urologists. We aim

to emphasize the diagnosis S-PHA in children with urological issue, and to propose a management

based on the published data.

MATERIAL AND METHODS

We retrospectively reviewed the cases of S-PHA related to urinary tract malformation from our

institution, and we performed a MEDLINE review from the literature.

RESULTS

Including the 4 cases from our institution, 116 cases of S-PHA associated with UTM were reviewed.

One hundred and six were aged below 6 months. A urinary tract infection (UTI) was associated in

105 cases (91 %). All types of UTM were represented. When no UTI is associated, S-PHA was

related to severe or bilateral UTM. In 89 cases (76.5 %), S-PHA resolved with medical treatment

associating electrolyte correction and appropriate antibiotic therapy. In cases of UTM needing im-

mediate surgery, the surgical intervention also resolved S-PHA.

CONCLUSIONS

S-PHA affects children with UTM under the age of 6 months. Associated UTI and bilateral or severe

UTM are at higher risk of developing S-PHA. Serum electrolyte balance must be checked in children

presenting UTM when undergoing urological surgery, and when presenting UTI, before 6 months of

age. Congenital adrenal hyperplasia must be suspected. S-PHA resolve after electrolyte correction

and UTI treatment and/or surgery.